Cystic Fibrosis Questions

Cystic Fibrosis Questions 1. Cystic fibrosis (CF) is a genetic disorder that causes the endocrine glands to work incorrectly. * False – exocrine works incorrectly 2. Select the systems below that are affected by cystic fibrosis: * o #A. Reproductive o #C. Respiratory o #D. Gastrointestinal o #F. Integumentary 3. You're educating the parents of an 8-month-old, who was recently diagnosed with cystic fibrosis, about the disease. You explain to the parents that the child has a gene mutation on the ____________. The gene that is specifically mutated is called?* o #B. exocrine glands; CFTR gene 4. Cystic fibrosis is an autosomal recessive genetic disorder. Which option below best describes what most likely happens for a child to develop this condition?* #D. Both parents, who are carriers of the mutated gene, each pass one mutated gene to the child 5. You're providing care to an 18-year-old male who has cystic fibrosis. Select all the possible complications this patient can experience due to cystic fibrosis:* o o #A. Blood glucose 255 mg/dL o #C. Hemoptysis o #D. Greasy, foul smelling stools o #G. Excessive mucus production o #H. Dyspnea #I. Coughing 6. You're discussing nutrition with your patient who has cystic fibrosis. You explain that it is very important the patient regularly takes fatsoluble vitamins. This includes:* o o #B. Vitamin D o #D. Vitamin K o #E. Vitamin E o #F. Vitamin A 7. About one hour after eating a meal, your patient, who has cystic fibrosis, starts to experience abdominal pain and bloating. Then two hours later the patient has a bowel movement. The patient's stool appears to be greasy and have a foul odor. Which medication below that is being taken by the patient is not providing a desirable outcome for this patient and needs to be re-addressed by the physician?* o #C. Pancrelipase 8. A patient with cystic fibrosis is diagnosed with pancreatic insufÏciency. As the nurse you know that the patient will be lacking:* o #A. Amylase o #C. Protease #E. Lipase 9. A patient completed a sweat test yesterday. The results are back and are 45 mmol/L. As the nurse you know this means:* o #C. The patient needs further testing because results are not conclusive. 10. The physician orders chest physiotherapy on your patient with cystic fibrosis. This is best performed:* o o #C. 1-2 hours after a meal 11. You're assisting a patient with performing chest physiotherapy. It is very important you have the patient ___________ during the therapy sessions.* o #C. huff cough 12. The physician gives an order for a patient with cystic fibrosis to use a positive expiratory pressure (PEP) device to help with airway clearance. As the nurse you will order which device from supply:* o #D. Flutter valve 13. A patient is scheduled to take Pancreatin. When will you administer this medication to the patient?* o #A. Right before all meals and snacks 14. A 2 year-old patient with cystic fibrosis is scheduled to take Pancrelipase. How will you administer this medication?* #C. orally with applesauce